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Concept information

Preferred term

void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

Created: 1986-08-28T00:00:00Z

Notation: 16735

gangliosidosis  

Definition

  • Information Enzim bozukluğuna ilgili olarak gangliyositlerin dokularda birikmesi, gelişme geriliği, baş ve bacak titremeleri, körlük, felç, gliozis, miyelin ve nöron kayıplarıyla belirgin bir grup kalıtsal lipit depo hastalığı. (tr)
  • Information La gangliosidose généralisée est une maladie des mammifères qui se transmet de manière autosomique récessive.

    Created: 6/12/24

    (fr)
  • Information Las gangliosidosis son un conjunto de enfermedades de almacenamiento lisosómico hereditarias debidas a un acúmulo de gangliósidos (un tipo de esfingolípidos), sobre todo en las neuronas

    Created: 6/12/24

    (es)
  • Information The gangliosidoses are a group of inherited metabolic diseases caused by a deficiency of the different proteins needed to break down lipids.

    Created: 6/12/24

Broader concept

In other languages

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2022-03-17T12:03:42Z

    Notation: 16735

    داء العقد

    Arabic

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2021-08-27T15:24:42Z

    Notation: 16735

    神经节苷脂贮积病

    Chinese

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2002-12-12T00:00:00Z

    Last modified: 2021-08-27T15:24:42Z

    Notation: 16735

    神经节苷脂沉积症
  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2003-03-27T00:00:00Z

    Notation: 16735

    gangliosidóza

    Czech

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 1987-04-01T00:00:00Z

    Last modified: 2021-05-24T17:34:42Z

    Notation: 16735

    gangliosidose

    French

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 1997-03-11T00:00:00Z

    Notation: 16735

    Gangliosidose

    German

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 1986-08-28T00:00:00Z

    Notation: 16735

    गैंगलिओसाईडोसिस

    Hindi

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2006-12-06T00:00:00Z

    Notation: 16735

    gangliosidosis

    Hungarian

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2006-10-27T00:00:00Z

    Notation: 16735

    Gangliosidosi

    Italian

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2005-08-09T00:00:00Z

    Notation: 16735

    ガングリオシド症、スフィンゴ脂質蓄積症、ガングリオシド蓄積症

    Japanese

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2009-12-02T00:00:00Z

    Notation: 16735

    갱그리오시도증

    Korean

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2007-04-20T00:00:00Z

    Notation: 16735

    گانگليوزيدوز

    Persian

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2006-12-19T00:00:00Z

    Notation: 16735

    Gangliozydoza

    Polish

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 1998-08-04T00:00:00Z

    Last modified: 2021-06-16T21:24:42Z

    Notation: 16735

    gangliosidose

    Portuguese

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2022-02-15T13:27:04

    Notation: 16735

    gangliozidoză

    Romanian

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2009-04-20T00:00:00Z

    Notation: 16735

    ганглиозидоз

    Russian

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2005-12-16T00:00:00Z

    Notation: 16735

    gangliozidóza

    Slovak

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 1990-06-18T00:00:00Z

    Notation: 16735

    Gangliosidosis

    Spanish

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2022-11-28T16:02:42Z

    Notation: 16735

    gangliosidosis

    Swahili

  • Information

    void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc

    Created: 2011-11-20T20:44:02Z

    Last modified: 2013-08-27T20:08:53Z

    Notation: 16735

    gangliyosidozis

    Turkish

URI

http://aims.fao.org/aos/agrovoc/c_16735

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