Concept information
Preferred term
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1986-08-28T00:00:00Z
Notation: 16735
Definition
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Enzim bozukluğuna ilgili olarak gangliyositlerin dokularda birikmesi, gelişme geriliği, baş ve bacak titremeleri, körlük, felç, gliozis, miyelin ve nöron kayıplarıyla belirgin bir grup kalıtsal lipit depo hastalığı.
(tr)Source: https://sozluk.gov.tr/
Created: 4/25/23
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La gangliosidose généralisée est une maladie des mammifères qui se transmet de manière autosomique récessive.
(fr)Created: 6/12/24
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Las gangliosidosis son un conjunto de enfermedades de almacenamiento lisosómico hereditarias debidas a un acúmulo de gangliósidos (un tipo de esfingolípidos), sobre todo en las neuronas
(es)Created: 6/12/24
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The gangliosidoses are a group of inherited metabolic diseases caused by a deficiency of the different proteins needed to break down lipids.
Created: 6/12/24
Broader concept
In other languages
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2022-03-17T12:03:42Z
Notation: 16735
Arabic
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2021-08-27T15:24:42Z
Notation: 16735
Chinese
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2002-12-12T00:00:00Z
Last modified: 2021-08-27T15:24:42Z
Notation: 16735
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2003-03-27T00:00:00Z
Notation: 16735
Czech
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1987-04-01T00:00:00Z
Last modified: 2021-05-24T17:34:42Z
Notation: 16735
French
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1997-03-11T00:00:00Z
Notation: 16735
German
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1986-08-28T00:00:00Z
Notation: 16735
Hindi
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2006-12-06T00:00:00Z
Notation: 16735
Hungarian
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2006-10-27T00:00:00Z
Notation: 16735
Italian
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2005-08-09T00:00:00Z
Notation: 16735
Japanese
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2009-12-02T00:00:00Z
Notation: 16735
Korean
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2007-04-20T00:00:00Z
Notation: 16735
Persian
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2006-12-19T00:00:00Z
Notation: 16735
Polish
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1998-08-04T00:00:00Z
Last modified: 2021-06-16T21:24:42Z
Notation: 16735
Portuguese
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2022-02-15T13:27:04
Notation: 16735
Romanian
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2009-04-20T00:00:00Z
Notation: 16735
Russian
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2005-12-16T00:00:00Z
Notation: 16735
Slovak
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 1990-06-18T00:00:00Z
Notation: 16735
Spanish
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2022-11-28T16:02:42Z
Notation: 16735
Swahili
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void:inDataset: http://aims.fao.org/aos/agrovoc/void.ttl#Agrovoc
Created: 2011-11-20T20:44:02Z
Last modified: 2013-08-27T20:08:53Z
Notation: 16735
Turkish